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KMID : 0391519950030010168
Journal of the Korean Child Neurology Society
1995 Volume.3 No. 1 p.168 ~ p.173
A Case of Recurrent Meningitis due to Mondini Dysplasia
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Abstract
Congenital inner ear malformations are divided into Michel dysplasia, Mondini dysplasia. Scheibe dysplasia and Alexander dysplasia. Mondini dysplasia results from arrested development during the seventh week of fetal life. Mondini dysplasia is
hereditary or spontaneously occurs and can be associated with sensory-neural hearing defects and recurrent meningitis.
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